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DeCS
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Descriptor English:
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Craniopharyngioma
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Descriptor Spanish:
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Craneofaringioma
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Descriptor Portuguese:
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Craniofaringioma
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Synonyms English:
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Craniopharyngioma, Adamantinous
Craniopharyngioma, Papillary
Rathke Pouch Tumor
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Tree Number:
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C04.557.465.625.200
C04.557.580.625.200
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Definition English:
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A benign pituitary-region neoplasm that originates from Rathke's pouch. The two major histologic and clinical subtypes are adamantinous (or classical) craniopharyngioma and papillary craniopharyngioma. The adamantinous form presents in children and adolescents as an expanding cystic lesion in the pituitary region. The cystic cavity is filled with a black viscous substance and histologically the tumor is composed of adamantinomatous epithelium and areas of calcification and necrosis. Papillary craniopharyngiomas occur in adults, and histologically feature a squamous epithelium with papillations. (From Joynt, Clinical Neurology, 1998, Ch14, p50) |
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Indexing Annotation English:
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coord IM with PITUITARY NEOPLASMS (IM)
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Allowable Qualifiers English:
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Record Number:
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3413
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Unique Identifier:
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D003397
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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